Syndrome of right isomerism: Ivemark syndrome
نویسندگان
چکیده
منابع مشابه
Ivemark Syndrome.
Ivemark syndrome or right atrial isomerism is a rare syndrome of asplenia / hyposplenia with malformation of heart and abnormal arrangement of internal organs of chest and abdomen and is classified under heterotaxy disorder. We describe here the case of a 14 year old boy diagnosed with asplenia, dextrocardia with double outlet right ventricle and midline liver.
متن کاملIvemark Syndrome- A Rare Syndrome with Constellation of Anatomical Defects
Ivemark syndrome is classified as a heterotaxy disorder or a laterality disorder. These terms refer to the failure of the internal organs of the chest and abdomen to be arranged in the proper location within the body. It is characterized by the absence (asplenia) or underdevelopment (hypoplasia) of the spleen, malformations of the heart and the abnormal arrangement of the internal organs of the...
متن کاملIvemark syndrome-a rare entity with specific anatomical features.
Ivemark syndrome (IS) is a rare embryological disorder which results from failure of development of the left-right asymmetry of organs. It is often associated with cardiac and other organ abnormalities, which are the usual causes of death in early neonatal life. We report a 3 months old girl with IS with dextrocardia, transposition of the great vessels, atrio-ventricular connection, total anoma...
متن کاملIvemark syndrome: bronchial compression from anomalous pulmonary venous anatomy
Ivemark syndrome is a heterotaxy syndrome which affects multiple organs and affects roughly 1 in every 6000 deliveries. Specifically, it can cause total anomalous pulmonary venous return and cardiac defects, which ultimately lead to decreased life expectancy. In order to better understand the nature of cardiac structures, CT angiogram has been heavily relied upon as it also allows for 3D recons...
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ژورنال
عنوان ژورنال: Journal of Mahatma Gandhi Institute of Medical Sciences
سال: 2018
ISSN: 0971-9903
DOI: 10.4103/jmgims.jmgims_31_17